hypoglycemia in gsd Type 1 or glycogen storage disorder Type 1 Von gierke disease

In von gierke disease which is Type 1 gsd due to the deficiency of glucose 6 phosphatase deficiency children usually have A Remarkable tolerance to low levels of blood glucose levels
they can tolerate blood glucose levels up to 20 milligram per decilitre without being symptomatic
The central nervous system is also adopted to utilise more Ketone bodies and lactase as alternative fuels

there is poor growth

Hyperglycemia is associated with acidosis, increased level of Beta hydroxybutyrate and lactate and hyperuricemia